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AbboMax
FKRP Polyclonal Antibody
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FIGURE: 1 / 1
FKRP Antibody (620-830) in WB
Western Blot: The whole mouse muscle tissue lysates were immunoblotted by Rabbit anti-FKRP (Cat#620-830) at 1:500 (Lane 1). The immunoreactive band is blocked by pre-incubation of immunizing peptide (lane 2). Observed a major immunoreactive band at molecular weight ~42 kDa.
Product Details
620-830
Applications
Tested Dilution
Publications
Product Specifications
Species Reactivity
Human,
Mouse,
Rat
Host/Isotype
Rabbit
/ IgG
Class
Polyclonal
Type
Antibody
Immunogen
A synthetic peptide corresponding to the C-terminus of human FKRP protein
Conjugate
Form
Liquid
Concentration
0.5 mg/mL
Purification
Antigen affinity chromatography
Storage buffer
PBS with proprietary stabilizer
Contains
0.01% sodium azide
Storage conditions
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Shipping conditions
Ambient (domestic); Wet ice (international)
Product Specific Information
Positive control: Muscle
Cellular location: Cytoplasmic.
Target Information
This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq, Oct 2008].
For Research Use Only. Not for use in diagnostic procedures. Not for resale without express authorization.
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Bioinformatics
Protein Aliases: Fukutin-related protein; Ribitol 5-phosphate transferase FKRP; Ribitol-5-phosphate transferase; unnamed protein product
Gene Aliases: A830029B19Rik; AI842067; AI847300; FKRP; FKTR; LGMD1I; LGMD2I; LGMDR9; MDC1C; MDDGA5; MDDGB5; MDDGC5
UniProt ID: (Human) Q9H9S5, (Mouse) Q8CG64
Entrez Gene ID: (Human) 79147, (Mouse) 243853, (Rat) 308390
glycoprotein biosynthetic process
protein processing
protein O-linked mannosylation
biological_process
eye development
in utero embryonic development
neuron migration
heart morphogenesis
respiratory system process
glycolytic process
protein glycosylation
creatine metabolic process
lipid metabolic process
muscle contraction
inflammatory response
central nervous system development
brain development
heart development
skeletal muscle tissue development
adult walking behavior
protein localization
glycoprotein metabolic process
response to xenobiotic stimulus
glial cell differentiation
gene expression
response to activity
protein import
pentose metabolic process
pentitol metabolic process
extracellular matrix organization
bone mineralization
maintenance of protein localization in endoplasmic reticulum
filtration diaphragm assembly
protein modification process
reelin-mediated signaling pathway
muscle cell differentiation
camera-type eye development
skeletal muscle tissue regeneration
protein kinase B signaling
neuromuscular process
striated muscle cell differentiation
protein tetramerization
response to glucocorticoid
localization of cell
skeletal muscle organ development
diaphragm development
muscle structure development
connective tissue development
basement membrane organization
oxygen metabolic process
response to alcohol
connective tissue replacement
skeletal muscle fiber differentiation
Disclaimer
Clicking the images or links will redirect you to a website hosted by BenchSci that provides third-party scientific content. Neither the content nor the BenchSci technology and processes for selection have been evaluated by us; we are providing them as-is and without warranty of any kind, including for use or application of the Thermo Fisher Scientific products presented.
Performance Guarantee
If an Invitrogen™ antibody doesn't perform as described on our website or datasheet,we'll replace the product at no cost to you, or provide you with a credit for a future purchase.*
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