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FKRP Antibody (PA5-99256) in IHC (P)
Immunohistochemistry analysis of FKRP in mouse heart tissue. The sample was formaldehyde fixed and a heat mediated antigen retrieval step in citrate buffer was performed. Samples were incubated with FKRP polyclonal antibody (Product # PA5-99256) using a dilution of 1:100 (4°C overnight) followed by HRP conjugated anti-Rabbit secondary antibody.
Product Details
PA5-99256
Applications
Tested Dilution
Publications
Product Specifications
Species Reactivity
Human,
Mouse,
Rat
Host/Isotype
Rabbit
/ IgG
Class
Polyclonal
Type
Antibody
Immunogen
A synthesized peptide derived from human FKRP(Accession Q9H9S5), corresponding to amino acid residues A8-A58.
Conjugate
Form
Liquid
Concentration
1 mg/mL
Purification
Affinity chromatography
Storage buffer
PBS, pH 7.4, with 50% glycerol
Contains
0.02% sodium azide
Storage conditions
-20°C
Shipping conditions
Wet ice
RRID
AB_2818189
Product Specific Information
Antibody detects endogenous levels of total FKRP.
Target Information
This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq, Oct 2008].
For Research Use Only. Not for use in diagnostic procedures. Not for resale without express authorization.
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Bioinformatics
Protein Aliases: Fukutin-related protein; Ribitol 5-phosphate transferase FKRP; Ribitol-5-phosphate transferase
Gene Aliases: A830029B19Rik; AI842067; AI847300; FKRP; LGMD1I; LGMD2I; MDC1C; MDDGA5; MDDGB5; MDDGC5
UniProt ID: (Human) Q9H9S5, (Mouse) Q8CG64
Entrez Gene ID: (Human) 79147, (Mouse) 243853, (Rat) 308390
Performance Guarantee
If an Invitrogen™ antibody doesn't perform as described on our website or datasheet,we'll replace the product at no cost to you, or provide you with a credit for a future purchase.*
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