|Tested species reactivity||Human, Rat|
|Host / Isotype||Goat / IgG|
|Immunogen||synthetic peptide PLAKDLLHPSPEE from N Terminus of the protein sequence according to NP_001021.|
|Storage buffer||TBS with 0.5% BSA|
|Contains||0.02% sodium azide|
|Storage Conditions||-20° C, Avoid Freeze/Thaw Cycles|
|Tested Applications||Dilution *|
|In Situ Hybridization (ISH) (ISH)||Assay-dependent|
|Western Blot (WB)||0.05-0.2 µg/ml|
* Suggested working dilutions are given as a guide only. It is recommended that the user titrate the product for use in their own experiment using appropriate negative and positive controls.
PA1-31888 detects MPS1 from human samples.
PA1-31888 has been successfully used in Western blot applications.
The PA1-31888 immunogen is: Synthetic peptide: PLAKDLLHPSPEE from N Terminus of the protein sequence according to NP_001021.
This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).
For Research Use Only. Not for use in diagnostic procedures. Not for resale without express authorization.