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|Tested species reactivity||Human|
|Host / Isotype||Rabbit / IgG|
|Immunogen||Recombinant fragment corresponding to a region within amino acids 2679 and 2871 of Human Fibrillin 1|
|Storage buffer||PBS, pH 7, with 40% glycerol|
|Storage Conditions||-20° C, Avoid Freeze/Thaw Cycles|
|Tested Applications||Dilution *|
|Western Blot (WB)||1:500-1:3000|
* Suggested working dilutions are given as a guide only. It is recommended that the user titrate the product for use in their own experiment using appropriate negative and positive controls.
PA5-27358 targets Fibrillin 1 in WB applications and shows reactivity with Human samples.
The PA5-27358 immunogen is recombinant fragment corresponding to a region within amino acids 2679 and 2871 of Human Fibrillin 1.
This gene encodes a member of the fibrillin family. The encoded protein is a large, extracellular matrix glycoprotein that serve as a structural component of 10-12 nm calcium-binding microfibrils. These microfibrils provide force bearing structural support in elastic and nonelastic connective tissue throughout the body. Mutations in this gene are associated with Marfan syndrome, isolated ectopia lentis, autosomal dominant Weill-Marchesani syndrome, MASS syndrome, and Shprintzen-Goldberg craniosynostosis syndrome.
For Research Use Only. Not for use in diagnostic procedures. Not for resale without express authorization.
ACMICD; FBN; fibrillin 15; Fibrillin-1; GPHYSD2; MASS; MFS1; OCTD; SGS; SSKS; WMS; WMS2
ACMICD; ECTOL1; FBN; FBN1; GPHYSD2; MASS; MFLS; MFS1; OCTD; SGS; SSKS; WMS; WMS2